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嗜铬细胞瘤是来源于神经嵴的产生儿茶酚胺的肿瘤。原发性心脏嗜铬细胞瘤是极为罕见的，全世界目前见于文献报道的仅为100例左右，北京协和医院心外科去年1月份成功进行了一例心脏嗜铬细胞瘤切除手术，患者为中年女性，肿瘤同时侵犯左右心房，其MIBG闪烁扫描的结果正常，但奥曲肽显像结果异常。肿瘤在体外循环下被成功切除。该病例报告已经发表在著名心胸外科专业杂志Annals of Thoracic Surgery上。

本文中的图表和表格

Fig 1. （A） 99m-Technetium-labeled hydrazinonicotinyl-Tyr3-octretide scintiscan demonstrated a focus of intense uptake on right side of heart silhouette. （B） Contrast-enhanced computed tomographic scan illustrated tumor （arrow） overlying interatrial groove. （LA = left atrium; RA = right atrium.）[p=30, 2, center]

Fig 2. Coronary angiogram demonstrated a tumor blush with 2 feeding vessels （white arrows） branching from left circumflex artery.[p=30, 2, center][img=360,387]http://w2.iiyi.com/bbs/uploadimg/z1357871845zakx8bt8.jpg[/img]

[p=30, 2, center]

Fig 3. Resected cardiac pheochromocytoma.

Primary Cardiac Pheochromocytoma Involving Both Right and Left Atria

Xingrong Liu, MD, Qi Miao, MD , Heng Zhang, MD, Chaoji Zhang, MD, Lihua Cao, MD, Guotao Ma, MD, Zhengpei Zeng, MD

Pheochromocytomas are catecholamine-producing paragangliomas derived from the neural crest. Primary cardiac pheochromocytoma is extremely rare. We describe a case of cardiac pheochromocytoma involving both right and left atria in a middle-aged woman. Metaiodobenzylguanidine （MIBG） scintiscan results were normal, but results from an octreotide scan were abnormal. The tumor was successfully resected using cardiopulmonary bypass （CPB）。

病例来源：爱爱医论坛